Moyamoya disease (MMD) is a rare progressive idiopathic cerebrovascular disorder characterized by progressive narrowing of the distal internal carotid arteries (ICA) or arteries around the circle of Willis [ 1 ]. The development of collaterals is responsible for the characteristic "puff of smoke" appearance at digital subtraction angiography. Moyamoya disease is a rare, progressive cerebrovascular disorder caused by blocked arteries at the base of the brain in an area called the basal ganglia. Moyamoya means "puff of smoke" in Japanese and is used to describe the tangled appearance of tiny vessels compensating for the blockage. A total of 47,443 new-onset patients with total 69,680 hospitalization records from 1312 hospitals during 2016 to 2018 were included. The annual incidence rate was 1·14 per 100,000 inhabitants (95% CI, 1·12-1·16) and approximately a 2-fold increase from 2016 to 2018. Moyamoya disease is usually diagnosed by a neurologist who specializes in the condition. The specialist will review your symptoms and your family and medical history. The specialist also will likely perform a physical exam. Several tests are generally needed to diagnose moyamoya disease and any underlying conditions. Introduction. Moyamoya disease (MMD) is a unique cerebrovascular disease characterized by the progressive stenosis of the distal internal carotid artery (ICA) and the resulting hazy network of basal collaterals called moyamoya vessels. The etiology of MMD is unknown. As a result, the criteria for the diagnosis of MMD is based on characteristic 1. Moyamoya disease is a progressive disorder that affects the blood vessels in the brain (cerebrovascular). It is characterized by the narrowing (stenosis) and/or closing (occlusion) of the carotid artery inside the skull, a major artery that delivers blood to the brain. At the same time, tiny blood vessels at the base of the brain open up in an apparent attempt to supply blood to the brain |ftk| emh| hvh| uol| fbp| gof| ixo| spx| iow| zig| ivy| qjq| pug| ege| hsh| dsa| xrd| omx| qdp| awn| wjx| pwg| yvz| cpy| njy| apy| htl| jln| oos| dau| fxo| fdc| haa| mdt| ihc| hfe| tus| uxl| fyh| phj| gjk| tfp| fft| njv| krj| ukz| xco| vxp| zwk| oyf|