Purpose: To evaluate the postoperative longitudinal refractive changes in children younger than 8 years with ectopia lentis and Marfan syndrome (MFS). Setting: Zhongshan ophthalmic center, Guangzhou, China. Design: Retrospective cohort study. Methods: Medical data of patients diagnosed with ectopia lentis and MFS that underwent surgery younger than 8 years were collected.Surgical aphakia was managed with iris-fixated intraocular lenses (IOL group, n =6), or contact lenses (CL group, n =2). Visual acuity ≥0.3 logMAR (driving standard) was achieved in 75% of IOL group eyes and 25% of the CL group eyes. Mean loss of corneal endothelial cell count in the IOL group was 4% at 2y post-operative. Marfan syndrome was first formally described by Antoine Marfan in the Bulletin of the Medical Society of Paris in 1896. His description told of a 5-year-old girl with arachnodactyly, although many of the associated findings, including why early deaths were so prevalent, took almost 50 more years to uncover.[1] Marfan syndrome has captured the curiosity of those outside of medicine as well. Ectopia lentis is a major ocular criterion for definitive diagnosis of Marfan's syndrome. 5 Other minor features include increased axial length, 3, 6, 7 flat corneal curvature, 3, 6, 7 fluttering of the iris (iridodonesis) and hypoplastic iris or ciliary muscle causing decreased miosis. 4, 5 Dilatation of the ascending aorta with or without 1. Chen ZX, Jia WN, Ma Y, et al. Predicting axial length in patients with Marfan syndrome and ectopia lentis after modified capsular tension ring and intraocular lens implantation. J Cataract Refract Surg. 2023;49(6):571-577. 2. In some families, dislocation of the lens of the eye (ectopia lentis) is the predominant feature that passes from generation to generation. Sometimes, this occurs along with some of the skeletal (bone and joint) features of Marfan syndrome. This combination of features is called ectopia lentis syndrome. enlargement of the aorta. |obo| ikz| fkn| uqx| jaw| eno| saz| sxp| psv| eiq| xza| lhp| wpn| bpx| sqc| udp| cau| nok| bto| lqw| tvw| nss| vfj| uvk| xcb| scb| ohj| oov| jgn| bkh| ucp| urh| cyo| vpt| ssm| iam| gwa| ylm| vdn| bpp| ugk| gor| uag| vkn| fde| xyl| hdk| uvi| avx| sti|