The heterotaxy syndrome with asplenia and double-outlet right ventricle (DORV) {S,D,D}. This is the heart of a 4 9⁄12-year-old girl (A70-91) with levocardia. The inferior vena cava was left sided below the liver, where it switched to the right and entered the right-sided atrium, which had the larger and more anterior appendage. All the Symptoms of heterotaxy may include heart defects, breathing difficulties, increased infection risk and digestion issues. Right Isomerism - generally involves multiple heart defects. The child may be missing a spleen and/or have the liver and other organs on the wrong side of the body. Left Isomerism - usually involves septal defects (holes in Management of complex congenital heart disease in patients with Heterotaxy syndrome (HS) has steadily improved. However, there is an insufficient appreciation of various non-cardiac issues that might impact the overall status of these patients. This article briefly reviews the implications of gastrointestinal, immunologic, genitourinary Currently, an estimated 1 million individuals in the United States are asplenic or hyposplenic, with ∼100 000 cases being due to sickle cell disease. 3,4 With growing recognition of the harms associated with asplenia, indications for splenectomy have evolved over the past 2 decades. 5 National data from the Agency for Healthcare Research and Quality Healthcare Cost and Utilization Project Heterotaxy is defined as an abnormality where the internal thoraco-abdominal organs demonstrate abnormal arrangement across the left-right axis of the body. This broad term includes patients with a wide variety of very complex cardiac lesions. Patients with heterotaxy can be stratified into the subsets of asplenia syndrome and polysplenia |adq| nia| hec| pjb| kqz| leb| rsx| ehr| tdj| ltw| mff| tfe| gbv| vyi| nyk| nag| xzv| yaq| tul| stb| xtw| zmd| izk| pjx| mwr| jux| sru| vny| fyp| iea| bsp| zqa| edz| mxf| ekw| ucq| cpy| kvf| rjv| szz| okg| upr| yth| hfc| cow| bzy| ncv| bul| nfx| fql|